Patient Diagnosed with Ebstein’s Anomaly
Ebstein’s Anomaly describes a congenital heart malformation where the tricuspid valve is downwardly displaced into the right ventricle. This is commonly described as an “atrialized right ventricle”. It is often associated with an atrial septal defect and various arrhythmias.
This patient was referred for periods of ventricular tachycardia. This patient has a history of hypertension and a permanent pacemaker.
In this echocardiogram, the aortic valve is mildly thickened but no significant stenosis is observed.
The septal tricuspid valve leaflet is downwardly displaced and the atrialized and true right atrium is moderately enlarged.
The true right ventricle is small and shows normal systolic function.
The interatrial septum appears intact, although no good subcostal views were obtained.
The left ventricle is of normal size and shows normal systolic function.
Colorflow and Doppler shows mild mitral, tricuspid, and pulmonary regurgitation and the aortic valve shows no significant stenosis.
As congenital heart diseases are rarely isolated, the sonographer should interrogate the IAS for any abnormal flows occurring in the atria.